Lipids | Hexb+/- | Hexb-/- |
---|---|---|
Total Gangliosides | 44.2 ± 1.2 | 39.7 ± 3.8 |
(nb = 5) | (n = 5) | |
Individual Gangliosidesc (n = 2) | ||
GM3 | 2.0, 2.5 | 2.8, 1.9 |
GM2 | n.d.d | 1.1, 1.0 |
LM1 | 1.5, 3.5 | 1.4, 0.8 |
GM1 | 0.7, 1.4 | 1.8, 1.0 |
GD3 | 0.6,0.6 | 0.6, 0.8 |
GD1a | 23.1, 23.9 | 23.8, 19.0 |
GT1a | 0.3, 0.3 | 1.0, 0.4 |
GD1b | 1.4, 1.8 | 1.6, 1.5 |
GT1b | 8.7, 7.7 | 8.6, 7.0 |
GQ1b | 6.5, 5.1 | 5.1, 4.5 |
Neutral | ||
Triglycerides | 38.2 ± 2.4 | 43.6 ± 5.0 |
Cholesterol | 9.9 ± 1.2 | 11.4 ± 1.5 |
Cerebrosides | 6.6 ± 0.5 | 6.7 ± 0.4 |
Phosphatidylethanolamine | 5.4 ± 0.4 | 6.0 ± 0.4 |
Phosphatidylcholine | 4.3 ± 0.3 | 3.8 ± 0.2 |
Sphingomyelin | 2.6 ± 0.3 | 2.4 ± 0.4 |
(n = 6) | (n = 6) | |
Acidic | ||
Sulfatides | 1.4 ± 0.1 | 1.4 ± 0.1 |
Phosphatidylserine | 3.2 ± 0.3 | 3.1 ± 0.1 |
Phosphatidylinositol | 0.4 ± 0.0 | 0.4 ± 0.0 |
(n = 5) | (n = 6) |